Pulmonary Artery Aneurysm as a Clue to Behcets Disease in a 7-Year-Old Boy

Abstract

Pulmonary artery aneurysm is a rare entity with a wide variety of underlying pathophysiological mechanisms. We report a 7-year-old boy who initially presented with suspected Lemierres syndrome (tonsillitis and jugular vein thrombosis). However, follow-up imaging studies showed progression of the thromboembolic changes into multiple dural venous structures as well as an aneurysm of the pulmonary artery, without respiratory symptoms. This rare combination of symptoms eventually led to the diagnosis of Behcets disease. In this report, we focus on the atypical presentation, the evolution of the clinical and radiological features and discuss the (radiological) clues, which led to the diagnosis.




Int J Clin Pediatr. 2015;4(4):189-192
doi: http://dx.doi.org/10.14740/ijcp231w