Extrahepatic Biliary Atresia With Cholestatic Jaundice and Hydrocephalus

Abstract

Biliary atresia is the most frequent cause of surgical jaundice in the late neonatal age group. Congenital extrahepatic biliary atresia and obstructive hydrocephalus is a rare association and not reported earlier in literature. We report a 2-month-old baby who presented with yellow discoloration of skin, high colored urine and clay colored stools since 20 days of life. Head size was apparently looking large with dilated veins over the scalp. The baby was diagnosed and treated as extrahepatic biliary atresia that led to cholestatic jaundice and cerebral aqueductal stenosis with hydrocephalus.




Int J Clin Pediatr. 2014;3(1):16-18
doi: http://dx.doi.org/10.14740/ijcp137w