Figure 1. Lower extremities/upper extremities: generalized osteopenia with cortical thickening and foci of sclerosis within the diaphyses of the long bones.
| International Journal of Clinical Pediatrics, ISSN 1927-1255 print, 1927-1263 online, Open Access |
| Article copyright, the authors; Journal compilation copyright, Int J Clin Pediatr and Elmer Press Inc |
| Journal website https://www.theijcp.org |
Case Report
Volume 9, Number 4, December 2020, pages 130-134
Insights Into Management of Camurati-Engelmann Disease: A Case Series of Three Siblings
Figure
Table
| Cumulative months of therapy | Therapy | FACES pain score | ESR (mm/h) | 6-min walk (m) | ||||||
|---|---|---|---|---|---|---|---|---|---|---|
| Case 1 | Case 2 | Case 3 | Case 1 | Case 2 | Case 3 | Case 1 | Case 2 | Case 3 | ||
| ESR: erythrocyte sedimentation rate. | ||||||||||
| 0 | Start | 4 | 10 | 6 | 56 | 74 | 42 | 354 | 422 | |
| 1 | Prednisone | 0 - 2 | 2 | 2 | ||||||
| 3 | Prednisone | 0 | 0 | 2 | 16 | 23 | 11 | |||
| 4 | Prednisone + losartan | 0 | 0 | 0 | ||||||
| 6 | Losartan | 4 | 2 | 2 | 15 | 18 | 10 | |||
| 7 | Losartan | 4 | 2 | 2 | ||||||
| 8 | No therapy | 8 | 4 | 6 | ||||||
| 9 | Deflazacort | 2 | 2 | 2 | ||||||
| 12 | Deflazacort | 8 | 4 | 2 | 54 | 26 | 33 | |||
| 15 | Deflazacort | 6 | 2 | 2 | 17 | 35 | 24 | |||
| 19 | Deflazacort | 2 | 0 - 2 | 2 | 280 | 415 | 503 | |||
| 23 | Deflazacort | 3 | 0 | 0 | ||||||